Abstract: We present an unusual case of cardiomyopathy in a two month
old male infant with a grade-I systolic murmur. Echocardiographic examination
disclosed left ventricular (LV), dysplasia with saw-tooth like inwards myocardial
projections extending from the lateral walls towards the LV cavity. There was mild LV
systolic dysfunction with ... read moreapical hypokinesia. Cardiovascular magnetic resonance
demonstrated in detail these cross bridging muscular projections originating from the
inferior interventricular septum and lateral LV wall, along with areas of hypokinesis
at the LV septum and apex in a noncoronary distribution, without any late gadolinium
enhancement. We have termed this condition saw-tooth cardiomyopathy because of the
very characteristic appearance.
Davlouros, Periklis, Peter G. Danias, Ageliki A. Karatza,
Maria G. Kiaffas, and Dimitrios Alexopoulos. "Saw-tooth cardiomyopathy." Journal of
Cardiovascular Magnetic Resonance 11, no. 1 (12, 2009):
1-3.